Cardiac arrhythmias in patients with surgical repair of Ebstein's anomaly

Preoperative, perioperative and postoperative arrhythmias in 52 consecutive patients who underwent operation for Ebstein's anomaly were reviewed. There were 25 male and 27 female patients (mean age 18 years, range 11 months to 64 years). Thirty-four patients had one or more documented arrhythmias preoperatively (18 had paroxysmal supraventricular tachycardia, 10 had paroxysmal atrial fibrillation or flutter, 13 had ventricular arrhythmia and 3 had high grade atrioventricular block). Seven patients without documented arrhythmias had a history typical of tachyarrhythmias. During the perioperative and early postoperative periods, 14 patients had atrial tachyarrhythmias and 8 had ventricular tachycardia or ventricular fibrillation. There were seven deaths between day 1 and 27 months after operation. Five of these deaths were sudden (all in male patients, aged 12 to 34 years), and four of the patients had had perioperative ventricular tachycardia or ventricular fibrillation. One patient was taking one antiarrhythmic agent and another patient was taking two at the time of sudden death. Of the 18 patients with paroxysmal supraventricular tachycardia and 9 patients with paroxysmal atrial fibrillation or flutter preoperatively who were followed up for a mean of 40 and 36 months, respectively, 22 and 33% continued to have symptomatic tachycardia. Of the 11 patients (mean age 9 years) without preoperative documentation or symptoms of arrhythmia, follow-up data were obtained (range 1 to 144 months, mean 31) in 9 patients. None died suddenly or developed symptomatic arrhythmia.

This article has been cited by other articles:

				E. P. Walsh Interventional Electrophysiology in Patients With Congenital Heart Disease Circulation, June 26, 2007; 115(25): 3224 - 3234. [Full Text] [PDF]

				E. P. Walsh and F. Cecchin Arrhythmias in Adult Patients With Congenital Heart Disease Circulation, January 30, 2007; 115(4): 534 - 545. [Full Text] [PDF]

				J. M. Stulak, J. A. Dearani, F. J. Puga, K. J. Zehr, H. V. Schaff, and G. K. Danielson Right-sided maze procedure for atrial tachyarrhythmias in congenital heart disease. Ann. Thorac. Surg., May 1, 2006; 81(5): 1780 - 1785. [Abstract] [Full Text] [PDF]

				A. Khositseth, G. K. Danielson, J. A. Dearani, T. M. Munger, and C. J. Porter Supraventricular tachyarrhythmias in Ebstein anomaly: Management and outcome J. Thorac. Cardiovasc. Surg., December 1, 2004; 128(6): 826 - 833. [Abstract] [Full Text] [PDF]

				C. L. Hancock Friesen, R. Chen, J. G. Howlett, and D. B. Ross Posterior annular plication: tricuspid valve repair in Ebstein's anomaly Ann. Thorac. Surg., June 1, 2004; 77(6): 2167 - 2171. [Abstract] [Full Text] [PDF]

				J. M. Chen, R. S. Mosca, K. Altmann, B. F. Printz, K. Targoff, P. A. Mazzeo, and J. M. Quaegebeur Early and medium-term results for repair of Ebstein anomaly J. Thorac. Cardiovasc. Surg., April 1, 2004; 127(4): 990 - 999. [Abstract] [Full Text] [PDF]

				S. M. Chauvaud, G. Brancaccio, and A. F. Carpentier Cardiac arrhythmia in patients undergoing surgical repair of Ebstein's anomaly Ann. Thorac. Surg., May 1, 2001; 71(5): 1547 - 1552. [Abstract] [Full Text] [PDF]

				V.V. Lazorishinets, M.D. Glagola, A.S. Stychinsky, M.N. Rudenko, and G.V. Knyshov Surgical treatment of Wolf-Parkinson-White syndrome during plastic operations in patients with Ebstein's anomaly Eur. J. Cardiothorac. Surg., October 1, 2000; 18(4): 487 - 490. [Abstract] [Full Text] [PDF]

				K. Durongpisitkul, C.-b. J. Porter, F. Cetta, K. P. Offord, J. M. Slezak, F. J. Puga, H. V. Schaff, G. K. Danielson, and D. J. Driscoll Predictors of Early- and Late-Onset Supraventricular Tachyarrhythmias After Fontan Operation Circulation, September 15, 1998; 98(11): 1099 - 1107. [Abstract] [Full Text] [PDF]

				D. A. Theodoro, G. K. Danielson, C.-b. J. Porter, and C. A. Warnes Right-Sided Maze Procedure for Right Atrial Arrhythmias in Congenital Heart Disease Ann. Thorac. Surg., January 1, 1998; 65(1): 149 - 154. [Abstract] [Full Text] [PDF]