Advertisement

Click here for more guidelines.

 
 




CME Topic Collections Past Issues Search Current Issue Home
     

J Am Coll Cardiol, 1992; 19:1041-1046
© 1992 by the American College of Cardiology Foundation
This Article
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Download to citation manager
Citing Articles
Right arrow Citing Articles via HighWire
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Celermajer, D.
Right arrow Articles by Deanfield, J.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Celermajer, D.
Right arrow Articles by Deanfield, J.

Outcome in neonates with Ebstein's anomaly

DS Celermajer, S Cullen, ID Sullivan, DJ Spiegelhalter, RK Wyse, and JE Deanfield

Cardiothoracic Unit, Hospital for Sick Children, London, England.

The presentation and outcome of 50 patients with neonatal Ebstein's anomaly seen from 1961 to 1990 were reviewed. The majority (88%) presented in the 1st 3 days of life; cyanosis (80%) was the most common presenting feature. Associated defects, present in 27 infants (54%), included pulmonary stenosis in 11 and atresia in 7. Nine patients (18%) died in the neonatal period; there were 15 late deaths (due to hemodynamic deterioration in 9, sudden death in 5 and a noncardiac cause in 1) at a mean age of 4.5 years (range 4 months to 19 years). Actuarial survival at 10 years was 61%. A new echocardiographic grade (1 to 4 in order of increasing severity of the defect) was devised with use of the ratio of the area of the right atrium and atrialized right ventricle to the area of the functional right ventricle and left heart chambers. Cardiac death occurred in 0 of 4 infants with grade 1, 1 (10%) of 10 with grade 2, 4 (44%) of 9 with grade 3 and 5 (100%) of 5 with grade 4. In a multivariate analysis of clinical and investigational features at presentation, echocardiographic grade of severity was the best independent predictor of death. Neonates with Ebstein's anomaly have a high early mortality rate and those surviving the 1st month of life remain at high risk of late hemodynamic deterioration or sudden death. Echocardiographic grading of severity of the defect permits prognostic stratification.


This article has been cited by other articles:


Home page
World Journal for Pediatric and Congenital Heart SurgeryHome page
C. J. Knott-Craig, S. P. Goldberg, J. A. Ballweg, and U. S. Boston
Surgical Decision Making in Neonatal Ebstein's Anomaly: An Algorithmic Approach Based on 48 Consecutive Neonates
World Journal for Pediatric and Congenital Heart Surgery, January 1, 2012; 3(1): 16 - 20.
[Abstract] [Full Text] [PDF]


Home page
World Journal for Pediatric and Congenital Heart SurgeryHome page
S. P. Goldberg, R. C. Jones, U. S. Boston, L. M. Haddad, G. T. Wetzel, T. K. Chin, and C. J. Knott-Craig
Current Trends in the Management of Neonates With Ebstein's Anomaly
World Journal for Pediatric and Congenital Heart Surgery, October 1, 2011; 2(4): 554 - 557.
[Abstract] [Full Text] [PDF]


Home page
J. Thorac. Cardiovasc. Surg.Home page
U. S. Boston, S. P. Goldberg, K. E. Ward, E. D. Overholt, T. Spentzas, T. K. Chin, and C. J. Knott-Craig
Complete repair of Ebstein anomaly in neonates and young infants: A 16-year follow-up
J. Thorac. Cardiovasc. Surg., May 1, 2011; 141(5): 1163 - 1169.
[Abstract] [Full Text] [PDF]


Home page
NeoreviewsHome page
U. T. Truong, S. R. Hintz, and T. A. Tacy
Ebstein Anomaly in the Fetus: Preparing for the Perfect Storm
NeoReviews, May 1, 2011; 12(5): e260 - e269.
[Abstract] [Full Text] [PDF]


Home page
J. Thorac. Cardiovasc. Surg.Home page
T. Shinkawa, A. C. Polimenakos, C. A. Gomez-Fifer, J. R. Charpie, J. C. Hirsch, E. J. Devaney, E. L. Bove, and R. G. Ohye
Management and long-term outcome of neonatal Ebstein anomaly
J. Thorac. Cardiovasc. Surg., February 1, 2010; 139(2): 354 - 358.
[Abstract] [Full Text] [PDF]


Home page
J Am Coll CardiolHome page
C. A. Warnes, R. G. Williams, T. M. Bashore, J. S. Child, H. M. Connolly, J. A. Dearani, P. del Nido, J. W. Fasules, T. P. Graham Jr, Z. M. Hijazi, et al.
ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Develop Guidelines on the Management of Adults With Congenital Heart Disease) Developed in Collaboration With the American Society of Echocardiography, Heart Rhythm Society, International Society for Adult Congenital Heart Disease, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons
J. Am. Coll. Cardiol., December 2, 2008; 52(23): e143 - e263.
[Full Text] [PDF]


Home page
CirculationHome page
C. A. Warnes, R. G. Williams, T. M. Bashore, J. S. Child, H. M. Connolly, J. A. Dearani, P. del Nido, J. W. Fasules, T. P. Graham Jr, Z. M. Hijazi, et al.
ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Develop Guidelines on the Management of Adults With Congenital Heart Disease): Developed in Collaboration With the American Society of Echocardiography, Heart Rhythm Society, International Society for Adult Congenital Heart Disease, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons
Circulation, December 2, 2008; 118(23): e714 - e833.
[Full Text] [PDF]


Home page
CirculationHome page
2006 WRITING COMMITTEE MEMBERS, R. O. Bonow, B. A. Carabello, K. Chatterjee, A. C. de Leon Jr, D. P. Faxon, M. D. Freed, W. H. Gaasch, B. W. Lytle, R. A. Nishimura, et al.
2008 Focused Update Incorporated Into the ACC/AHA 2006 Guidelines for the Management of Patients With Valvular Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the 1998 Guidelines for the Management of Patients With Valvular Heart Disease): Endorsed by the Society of Cardiovascular Anesthesiologists, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons
Circulation, October 7, 2008; 118(15): e523 - e661.
[Full Text] [PDF]


Home page
J Am Coll CardiolHome page
R. O. Bonow, B. A. Carabello, K. Chatterjee, A. C. de Leon Jr, D. P. Faxon, M. D. Freed, W. H. Gaasch, B. W. Lytle, R. A. Nishimura, P. T. O'Gara, et al.
2008 Focused Update Incorporated Into the ACC/AHA 2006 Guidelines for the Management of Patients With Valvular Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the 1998 Guidelines for the Management of Patients With Valvular Heart Disease) Endorsed by the Society of Cardiovascular Anesthesiologists, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic Surgeons
J. Am. Coll. Cardiol., September 23, 2008; 52(13): e1 - e142.
[Full Text] [PDF]


Home page
J. Thorac. Cardiovasc. Surg.Home page
B. L. Reemtsen, A. C. Polimenakos, B. T. Fagan, W. J. Wells, and V. A. Starnes
Fate of the right ventricle after fenestrated right ventricular exclusion for severe neonatal Ebstein anomaly.
J. Thorac. Cardiovasc. Surg., December 1, 2007; 134(6): 1406 - 1412.
[Abstract] [Full Text] [PDF]


Home page
Eur Heart JHome page
L. Kapusta, R. M. Eveleigh, S. E. Poulino, M. E. Rijlaarsdam, G. J. du Marchie Sarvaas, J. L. Strengers, T. Delhaas, C. L. de Korte, T. Feuth, and W. A. Helbing
Ebstein's anomaly: factors associated with death in childhood and adolescence: a multi-centre, long-term study
Eur. Heart J., November 1, 2007; 28(21): 2661 - 2666.
[Abstract] [Full Text] [PDF]


Home page
Ann. Thorac. Surg.Home page
C. J. Knott-Craig, S. P. Goldberg, E. D. Overholt, E. V. Colvin, and J. K. Kirklin
Repair of Neonates and Young Infants With Ebstein's Anomaly and Related Disorders
Ann. Thorac. Surg., August 1, 2007; 84(2): 587 - 593.
[Abstract] [Full Text] [PDF]


Home page
CirculationHome page
C. H. Attenhofer Jost, H. M. Connolly, J. A. Dearani, W. D. Edwards, and G. K. Danielson
Ebstein's Anomaly
Circulation, January 16, 2007; 115(2): 277 - 285.
[Full Text] [PDF]


Home page
J. Thorac. Cardiovasc. Surg.Home page
B. L. Reemtsen, B. T. Fagan, W. J. Wells, and V. A. Starnes
Current surgical therapy for Ebstein anomaly in neonates
J. Thorac. Cardiovasc. Surg., December 1, 2006; 132(6): 1285 - 1289.
[Abstract] [Full Text] [PDF]


Home page
J Am Coll CardiolHome page
R. O. Bonow, B. A. Carabello, K. Chatterjee, A. C. de Leon Jr, D. P. Faxon, M. D. Freed, W. H. Gaasch, B. W. Lytle, R. A. Nishimura, P. T. O'Gara, et al.
ACC/AHA 2006 Guidelines for the Management of Patients With Valvular Heart Disease: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the 1998 Guidelines for the Management of Patients With Valvular Heart Disease) Developed in Collaboration With the Society of Cardiovascular Anesthesiologists Endorsed by the Society for Cardiovascular Angiography and Interventions and the Society of Thoracic Surgeons
J. Am. Coll. Cardiol., August 1, 2006; 48(3): e1 - e148.
[Full Text] [PDF]


Home page
Ann. Thorac. Surg.Home page
M. Watanabe, Y. Harada, T. Takeuchi, G. Satomi, and S. Yasukouchi
Modified Starnes operation for neonatal Ebstein's anomaly
Ann. Thorac. Surg., September 1, 2002; 74(3): 916 - 917.
[Abstract] [Full Text] [PDF]


Home page
Ann. Thorac. Surg.Home page
C. J. Knott-Craig, E. D. Overholt, K. E. Ward, J. M. Ringewald, S. S. Baker, and J. D. Razook
Repair of Ebstein's anomaly in the symptomatic neonate: an evolution of technique with 7-year follow-up
Ann. Thorac. Surg., June 1, 2002; 73(6): 1786 - 1793.
[Abstract] [Full Text] [PDF]


Home page
J Am Coll CardiolHome page
F. Attie, M. Rosas, N. Granados, C. Zabal, A. Buendia, and J. Calderon
Surgical treatment for secundum atrial septal defects in patients >40 years old: A randomized clinical trial
J. Am. Coll. Cardiol., December 1, 2001; 38(7): 2035 - 2042.
[Abstract] [Full Text] [PDF]


Home page
Ann. Thorac. Surg.Home page
C. J. Knott-Craig, E. D. Overholt, K. E. Ward, and J. D. Razook
Neonatal repair of Ebstein's anomaly: indications, surgical technique, and medium-term follow-up
Ann. Thorac. Surg., May 1, 2000; 69(5): 1505 - 1510.
[Abstract] [Full Text] [PDF]


Home page
Ann. Thorac. Surg.Home page
M. Endo, M. Ohmi, K. Sato, T. Tanaka, H. Kakizawa, and K. Tabayashi
Tricuspid Valve Closure for Neonatal Ebstein's Anomaly
Ann. Thorac. Surg., February 1, 1998; 65(2): 540 - 540.
[Abstract] [Full Text] [PDF]



 
  CME Topic Collections Past Issues Search Current Issue Home

Advertisement