Please click here to obtain permission to reproduce this image.

Click on image to view larger version.


Figure 4


Figure 4 6MW Tests Were Obtained for 13 of 22 Patients at Baseline and After 6 Months

Overall, there was no change in 6-min walk distance (6MWD) from baseline (397 m) to 6 months (428 m); however, 6MWD did increase by >10% in 5, was unchanged in 7, and decreased by >10% in 1 child.