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Figure 4 Scimitar Syndrome in a 3-Month-Old Boy

Contrast-enhanced angiograms, reformatted in slanted coronal planes, show the scimitar vein draining most of the right lung to the inferior vena cava (IVC). (A) The scimitar vein shows severe stenosis as it connects to the IVC. Note the high signal intensity flow in the IVC. (B) A small right lower pulmonary vein (RLPV) and the left pulmonary veins (LUPV and LLPV) have normal connections to the left atrium (LA). The LUPV is stenosed. A small aberrant arterial branch arises from the abdominal descending aorta (Ao) to supply the posterior basal part of the right lower lobe. The right lung volume is smaller than the left lung volume. In this case, the right pulmonary artery (RPA) is not hypoplastic. LLPV = left lower pulmonary vein; LUPV = left upper pulmonary vein; PA = main pulmonary artery; RA = right atrium.