Click on image to view larger version.

Figure 1 Bronchopulmonary arterial anatomy in pulmonary atresia associated with ventricular septal defect (PAVSD) is characterized by a continuous morphologic spectrum, but our definition of major aortopulmonary collateral arteries (MAPCA) patients is supported by the obvious polarization of those in the non-MAPCA group (closed circles) and those in the MAPCA group (open circles). There is a strong negative correlation (r² = 0.8; p < 0.001) between increasing number of bronchopulmonary segments supplied by the native pulmonary arteries and decreasing number of bronchopulmonary segments with abnormal supply. Abnormal supply = number of dual supplied segments + number of unperfused segments + number of collateral supplied segments; PA = pulmonary artery; RVOT = right ventricular outflow tract.